Back متلازمة إيفانز Arabic Evans sindromu Azerbaijani Evans-Syndrom German Síndrome de Evans Spanish Syndrome d'Evans French Sindrome di Evans Italian Evanso sindromas Lithuanian Syndroom van Evans Dutch Zespół Evansa Polish Hội chứng Evans Vietnamese

Evans syndrome

Evans syndrome
SpecialtyHematology Edit this on Wikidata

Evans syndrome is an autoimmune disease in which an individual's immune system attacks their own red blood cells and platelets, the syndrome can include immune neutropenia.[1][2] These immune cytopenias may occur simultaneously or sequentially.[1][3]

Its overall phenotype resembles a combination of autoimmune hemolytic anemia and immune thrombocytopenic purpura.[1][4][5] Autoimmune hemolytic anemia is a condition in which the red blood cells that normally carry oxygen are destroyed by an autoimmune process. Immune thrombocytopenic purpura is a condition in which platelets are destroyed by an autoimmune process. Platelets are a component of blood that contribute to the formation of blood clots in the body to prevent bleeding.

The syndrome was first described in 1951 by R. S. Evans and colleagues.[1]

  1. ^ a b c d "Evans Syndrome". NORD (National Organization for Rare Disorders). Retrieved 2022-03-15.
  2. ^ "Evans syndrome". Genetic and Rare Diseases Information Center. Retrieved 2018-04-17.
  3. ^ Norton A, Roberts I (2006). "Management of Evans syndrome". Br. J. Haematol. 132 (2): 125–37. doi:10.1111/j.1365-2141.2005.05809.x. PMID 16398647. S2CID 7633446.
  4. ^ Cite error: The named reference pmid31292991 was invoked but never defined (see the help page).
  5. ^ Michel M; Chanet V; Dechartres A; Morin A-S; Piette J-C; Cirasino L; Emilia G; Zaja F; Ruggeri M; Andrès E; Bierling P; Godeau B; Rodeghiero F (2009). "The spectrum of Evans syndrome in adults: new insight into the disease based on the analysis of 68 cases". Blood. 114 (15): 3167–3172. doi:10.1182/blood-2009-04-215368. PMID 19638626.

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